Carcinosarcoma of the Choledochal Cyst

We report the case of a 19-year-old young man with choledoch carcinosarcoma secondary to anastomosis of choledochal cyst and jejunum. The patient suffered from the choledochal cyst and received anastomosis of choledochal cyst and jejunum at 4-year-old. The patient was hospitalized because of abdominal pain, fever and obstructive jaundice. The imaging examination showed a huge heterogeneous tumor located in the hilar area with dilatation of intra hepatic bile duct. Resections of choledoch cyst and jejunum loop associated with pancreaticoduodenectomy were performed during the operation. Carcinosarcoma was pathologically diagnosed after the operation. Pelvic metastases were diagnosed 8 months postoperatively and sigmoid colostomy was therefore performed. The patient died 4 months later.